R. Morgan, S. Mcnally, A. M. Conroy, R. Hardiman, O. Costello et al., Use of Sniff Nasal-Inspiratory Force to Predict Survival in Amyotrophic Lateral Sclerosis, American Journal of Respiratory and Critical Care Medicine, vol.171, issue.3, pp.269-74, 2005.
DOI : 10.1164/rccm.200403-314OC

I. Arnulf, T. Similowski, and F. Salachas, Sleep Disorders and Diaphragmatic Function in Patients with Amyotrophic Lateral Sclerosis, American Journal of Respiratory and Critical Care Medicine, vol.161, issue.3, pp.849-56, 2000.
DOI : 10.1164/ajrccm.161.3.9805008

J. Gil, B. Funalot, and A. Verschueren, Causes of death amongst French patients with amyotrophic lateral sclerosis: a prospective study, European Journal of Neurology, vol.298, issue.Suppl. 1, pp.1245-51, 2008.
DOI : 10.1111/j.1468-1331.2008.02307.x

T. Heiman-patterson and R. Miller, NIPPV: A treatment for ALS whose time has come, Neurology, vol.67, issue.5, pp.736-743, 2006.
DOI : 10.1212/01.wnl.0000238978.69141.57

P. Andersen, S. Abrahams, and G. Borasio, EFNS guidelines on the clinical management of amyotrophic lateral sclerosis (MALS)--revised report of an EFNS task force, Eur J Neurol, vol.19, pp.360-75, 2012.

S. Bourke, R. Bullock, T. Williams, P. Shaw, and G. Gibson, Noninvasive ventilation in ALS: Indications and effect on quality of life, Neurology, vol.61, issue.2, pp.171-178, 2003.
DOI : 10.1212/01.WNL.0000076182.13137.38

S. Bourke, M. Tomlinson, T. Williams, R. Bullock, P. Shaw et al., Effects of non-invasive ventilation on survival and quality of life in patients with amyotrophic lateral sclerosis: a randomised controlled trial, The Lancet Neurology, vol.5, issue.2, pp.140-147, 2006.
DOI : 10.1016/S1474-4422(05)70326-4

L. Aboussouan, S. Khan, D. Meeker, K. Stelmach, and H. Mitsumoto, Effect of Noninvasive Positive-Pressure Ventilation on Survival in Amyotrophic Lateral Sclerosis, Annals of Internal Medicine, vol.127, issue.6
DOI : 10.7326/0003-4819-127-6-199709150-00006

L. Coco, D. Marchese, S. Pesco, M. , L. Bella et al., Noninvasive positive-pressure ventilation in ALS: predictors of tolerance and survival Survival of patients on home mechanical ventilation: a nationwide prospective study Prognostic value of efficiently correcting nocturnal desaturations after one month of non-invasive ventilation in amyotrophic lateral sclerosis: a retrospective monocentre observational cohort study Patient-ventilator asynchrony with nocturnal noninvasive ventilation in ALS Proposal for a systematic analysis of polygraphy or polysomnography for identifying and scoring abnormal events occurring during non-invasive ventilation Identifying who will benefit from non-invasive ventilation in amyotrophic lateral sclerosis/motor neurone disease in a clinical cohort El Escorial revisited: revised criteria for the diagnosis of amyotrophic lateral sclerosis, Neurology Respir Med Amyotroph Lateral Scler Frontotemporal Degener Neurology Thorax J Neurol Neurosurg Amyotroph Lateral Scler Other Motor Neuron Disord, vol.671011477671, issue.14, pp.761-51074, 2000.

V. Cordesse, F. Sidorok, P. Schimmel, J. Holstein, V. Meininger et al., Coordinated care affects hospitalization and prognosis in amyotrophic lateral sclerosis: a cohort study Ambulatory adaptation of non-invasive ventilation in motor neuron disease: where limits of effectiveness end--reply, BMC Health Serv Res, vol.15, 2015.

J. Janssens, J. Borel, J. Pepin, R. Berry, R. Budhiraja et al., Rules for scoring respiratory events in sleep: update of the 2007 AASM Manual for the Scoring of Sleep and Associated Events. Deliberations of the Sleep Apnea Definitions Task Force of the American Academy of Sleep Medicine Reliability of Apnea-Hypopnea Index Measured by a Home Bi-Level Pressure Support Ventilator Versus a Polysomnographic Assessment Oral appliance to assist non-invasive ventilation in a patient with amyotrophic lateral sclerosis Effects of non-invasive ventilation on objective sleep and nocturnal respiration in patients with amyotrophic lateral sclerosis Otolaryngologic presentations of amyotrophic lateralsclerosis, 24. DePaul R, Abbs JH, Caligiuri M, Gracco VL, Brooks BR. Hypoglossal, trigeminal, and facial motoneuron involvement in amyotrophic lateral sclerosis, pp.438-45597, 1988.

R. Kent, R. Sufit, and J. Rosenbek, Speech Deterioration in Amyotrophic Lateral Sclerosis, Journal of Speech Language and Hearing Research, vol.34, issue.6, pp.1269-75, 1991.
DOI : 10.1044/jshr.3406.1269

H. Tankisi, M. Otto, K. Pugdahl, A. Fuglsang-frederiksen, R. Kimoff et al., Spontaneous electromyographic activity of the tongue in amyotrophic lateral sclerosis Upper airway sensation in snoring and obstructive sleep apnea Vocal cord dysfunction in amyotrophic lateral sclerosis: four cases and a review of the literature Influence of lung volume in sleep apnoea al. Lung volume and continuous positive airway pressure requirements in obstructive sleep apnea, Muscle Nerve Am J Respir Crit Care Med Arch Neurol Thorax Am J Respir Crit Care Med, vol.481646644172, issue.28, pp.296-8250, 1989.

S. Redolfi, D. Yumino, and P. Ruttanaumpawan, Relationship between Overnight Rostral Fluid Shift and Obstructive Sleep Apnea in Nonobese Men, American Journal of Respiratory and Critical Care Medicine, vol.179, issue.3, pp.241-247, 2009.
DOI : 10.1164/rccm.200807-1076OC

W. Mezzanotte, D. Tangel, and D. White, Waking genioglossal electromyogram in sleep apnea patients versus normal controls (a neuromuscular compensatory mechanism)., Journal of Clinical Investigation, vol.89, issue.5, pp.1571-1580, 1992.
DOI : 10.1172/JCI115751

Y. Lo, A. Jordan, and A. Malhotra, Influence of wakefulness on pharyngeal airway muscle activity, Thorax, vol.62, issue.9, pp.799-805, 2007.
DOI : 10.1136/thx.2006.072488

C. Launois, V. Attali, and M. Georges, Cortical Drive to Breathe during Wakefulness in Patients with Obstructive Sleep Apnea Syndrome Effects of nasal positive-pressure hyperventilation on the glottis in normal sleeping subjects Nonchemical influence of inspiratory pressure support on inspiratory activity in humans, J Appl Physiol J Appl Physiol, vol.7985, issue.36, pp.186-932169, 1985.

N. Hopkinson, T. Sharshar, M. Dayer, F. Lofaso, J. Moxham et al., The effect of acute non-invasive ventilation on corticospinal pathways to the respiratory muscles in chronic obstructive pulmonary disease Cortical drive to breathe in amyotrophic lateral sclerosis: a dyspnoea-worsening defense The effect of sleep onset on upper airway muscle activity in patients with sleep apnoea versus controls, Respir Physiol Neurobiol Eur Respir J J Physiol, vol.183564, issue.39, pp.41-7549, 2005.

. Funding, This work was supported by the programInvestissement d'Avenir ANR-10-AIHU 06 of the French Government » Competing Interests statement : The authors have no conflict of interest to declare Contributorship Statement 1

V. Trosini-desert, François Salachas (1,3,4,5), 2005.